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EPONYM

Sweet syndrome

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Abstract

Sweet syndrome, also referred to as acute febrile neutrophilic dermatosis, is characterized by tender, red inflammatory nodules or papules that occur in association with infection, malignancy, connective tissue disease, or following exposure to certain drugs. Although drug-induced Sweet syndrome is rare, granulocyte colony-stimulating factor, all-trans-retinoic acid, and miscellaneous drugs have been implicated in causing this disorder in adults. In pediatric patients, granulocyte colony-stimulating factor, all-trans-retinoic acid, trimethoprim-sulfamethoxazole, and azathioprine have been implicated as potential causes of drug-induced Sweet syndrome. To date, six cases, including the patient reported here, have been reported in children.

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Abbreviations

SS:

Sweet syndrome

c-ANCA:

c-type anti-neutrophil cytoplasmic antibody

TPMT:

Thiopurine methyltransferase

GCSF:

Granulocyte colony-stimulating factor

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  1. Department of Pediatrics, Samsung Medical Center, Sungkyunkwan University School of Medicine, 50 Irwon-dong, Gangnam-gu, Seoul, 135-710, South Korea

    Mi Jin Kim & Yon Ho Choe

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  1. Mi Jin Kim
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Correspondence to Yon Ho Choe.

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Kim, M.J., Choe, Y.H. EPONYM. Eur J Pediatr 169, 1439–1444 (2010). https://doi.org/10.1007/s00431-010-1201-z

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