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Review of surgical and anesthetic management for esophageal atresia with tracheoesophageal fistula, unilateral pulmonary agenesis and dextrocardia

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Abstract

Association of unilateral severe pulmonary atresia or agenesis and esophageal atresia (EA) with or without tracheoesophageal fistula (TEF) and dextrocardia is a rare and highly lethal combination. We report a case of a full-term female infant who had EA with TEF, right lung agenesis, and dextrocardia. Repair of the fistula took place on day of life 3. We describe anesthetic and surgical concerns of this patient’s case which are keys to a good operative outcome as well as follow-up for the patient.

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Authors and Affiliations

  1. Department of Surgery, Children’s Mercy Hospital, 2401 Gillham Road, Kansas City, MO, 64108, USA

    Rebecca M. Rentea, Tolulope A. Oyetunji & Richard J. Hendrickson

  2. Department of Anesthesiology, Children’s Mercy Hospital, Kansas City, MO, USA

    John Erkmann

  3. Department of Radiology, Children’s Mercy Hospital, Kansas City, MO, USA

    Joshua Q. Knowlton

Authors
  1. Rebecca M. Rentea
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  2. Tolulope A. Oyetunji
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  3. John Erkmann
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  4. Joshua Q. Knowlton
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  5. Richard J. Hendrickson
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Correspondence to Rebecca M. Rentea.

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Rentea, R.M., Oyetunji, T.A., Erkmann, J. et al. Review of surgical and anesthetic management for esophageal atresia with tracheoesophageal fistula, unilateral pulmonary agenesis and dextrocardia. Pediatr Surg Int 33, 817–821 (2017). https://doi.org/10.1007/s00383-017-4090-7

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  • DOI: https://doi.org/10.1007/s00383-017-4090-7

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