Abstract
Rhabdomyosarcoma is the most common tumor of the biliary tract in children. Although some features at preoperative radiographic studies (ultrasound, CT, MRI) may be suggestive of BT-RMS, until few years ago the final diagnosis was obtained by either operative or transcutaneous biopsy, thus exposing to a risk of regional dissemination. More recent and still anecdotal, is the histological diagnosis on tissue obtained by transluminal biopsy either during transhepatic cholangiography or endoscopic retrograde cholangio-pancreatography (ERCP), the latter having the major advantage of a much lower risk of loco-regional dissemination. We present two cases of BT-RMS that were histologically diagnosed by intracholedocal biopsy performed during ERCP, after being suspected at conventional imaging.
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Abbreviations
- BT:
-
Biliary tract
- CBD:
-
Common bile duct
- CT:
-
Computed tomography
- ERCP:
-
Endoscopic retrograde cholangio-pancreatography
- MRI:
-
Magnetic resonance imaging
- RMS:
-
Rhabdomyosarcoma
- US:
-
Ultrasonography
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Scottoni, F., De Angelis, P., Dall’Oglio, L. et al. ERCP with intracholedocal biopsy for the diagnosis of biliary tract rhabdomyosarcoma in children. Pediatr Surg Int 29, 659–662 (2013). https://doi.org/10.1007/s00383-013-3282-z
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DOI: https://doi.org/10.1007/s00383-013-3282-z