Child's Nervous System

, Volume 24, Issue 4, pp 515–520

Relief of severe retro-orbital pain and vision improvement after optic-nerve decompression in polyostotic fibrous dysplasia: case report and review of the literature

Authors

  • S. J. C. Sammut
    • Department of NeurosurgeryRoyal Liverpool Children’s Hospital
  • J. Kandasamy
    • Department of NeurosurgeryRoyal Liverpool Children’s Hospital
  • W. Newman
    • Department of OphthalmologyRoyal Liverpool Children’s Hospital
  • A. Sinha
    • Department of NeurosurgeryRoyal Liverpool Children’s Hospital
  • J. Ross
    • Department of NeurosurgeryRoyal Liverpool Children’s Hospital
  • J. C. Blair
    • Department of EndocrinologyRoyal Liverpool Children’s Hospital
    • Department of NeurosurgeryRoyal Liverpool Children’s Hospital
Case Report

DOI: 10.1007/s00381-007-0543-y

Cite this article as:
Sammut, S.J.C., Kandasamy, J., Newman, W. et al. Childs Nerv Syst (2008) 24: 515. doi:10.1007/s00381-007-0543-y

Abstract

Introduction

We describe a case of a 9-year-old girl who developed progressive severe retro-orbital pain and partial visual loss in association with left optic-nerve compression due to polyostotic fibrous dysplasia of the skull.

Materials and methods

Intradural decompression of the optic nerve resulted in immediate and complete resolution of the pain as well as a vast visual improvement.

Conclusion

In cases of fibrous dysplasia of the skull with evidence of optic-nerve compression, relief of retro-orbital pain should be an additional consideration when deciding to proceed with surgical management.

Keywords

Optic nerveDecompressionFibrous dysplasia of bonePainVisionMagnetic resonance imaging

Copyright information

© Springer-Verlag 2007