Case Report

Child's Nervous System

, Volume 24, Issue 4, pp 515-520

Relief of severe retro-orbital pain and vision improvement after optic-nerve decompression in polyostotic fibrous dysplasia: case report and review of the literature

  • S. J. C. SammutAffiliated withDepartment of Neurosurgery, Royal Liverpool Children’s Hospital
  • , J. KandasamyAffiliated withDepartment of Neurosurgery, Royal Liverpool Children’s Hospital
  • , W. NewmanAffiliated withDepartment of Ophthalmology, Royal Liverpool Children’s Hospital
  • , A. SinhaAffiliated withDepartment of Neurosurgery, Royal Liverpool Children’s Hospital
  • , J. RossAffiliated withDepartment of Neurosurgery, Royal Liverpool Children’s Hospital
  • , J. C. BlairAffiliated withDepartment of Endocrinology, Royal Liverpool Children’s Hospital
  • , P. MayAffiliated withDepartment of Neurosurgery, Royal Liverpool Children’s Hospital Email author 

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Abstract

Introduction

We describe a case of a 9-year-old girl who developed progressive severe retro-orbital pain and partial visual loss in association with left optic-nerve compression due to polyostotic fibrous dysplasia of the skull.

Materials and methods

Intradural decompression of the optic nerve resulted in immediate and complete resolution of the pain as well as a vast visual improvement.

Conclusion

In cases of fibrous dysplasia of the skull with evidence of optic-nerve compression, relief of retro-orbital pain should be an additional consideration when deciding to proceed with surgical management.

Keywords

Optic nerve Decompression Fibrous dysplasia of bone Pain Vision Magnetic resonance imaging