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Imaging neonates and children with Pierre Robin sequence before and after mandibular distraction osteogenesis: what the craniofacial surgeon wants to know

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Abstract

Pierre Robin sequence is characterized by micrognathia and glossoptosis causing upper airway obstruction. Mandibular distraction osteogenesis is a mandibular lengthening procedure performed in neonates and children with Pierre Robin sequence to alleviate airway compromise. This pictorial review demonstrates the role of imaging in the preoperative and postoperative assessment of these children. It is important for pediatric radiologists to know what information about the mandible and airway the craniofacial surgeon needs from preoperative imaging and to identify any complications these children may encounter after surgery.

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Acknowledgments

We thank Margie Bessette Baker for providing reformatted images.

Conflicts of interest

Dr. A.D. Denny is a paid consultant for Stryker Corp., a medical equipment company.

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Author notes

  1. Markus G. Zei

    Present address: St. Louis University School of Medicine, St. Louis, MO, USA

Authors and Affiliations

  1. Department of Imaging, Medical College of Wisconsin, Children’s Hospital of Wisconsin, P.O. Box 1997, MS 721, Milwaukee, WI, 53211-1997, USA

    Arthur B. Meyers

  2. Medical College of Wisconsin, Milwaukee, WI, USA

    Markus G. Zei

  3. Department of Plastic Surgery, Medical College of Wisconsin, Children’s Hospital of Wisconsin, Milwaukee, WI, USA

    Arlen D. Denny

Authors
  1. Arthur B. Meyers
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  2. Markus G. Zei
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  3. Arlen D. Denny
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Correspondence to Arthur B. Meyers.

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Meyers, A.B., Zei, M.G. & Denny, A.D. Imaging neonates and children with Pierre Robin sequence before and after mandibular distraction osteogenesis: what the craniofacial surgeon wants to know. Pediatr Radiol 45, 1392–1402 (2015). https://doi.org/10.1007/s00247-015-3323-y

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  • DOI: https://doi.org/10.1007/s00247-015-3323-y

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