Abstract
This report describes a rare case of Tetralogy of Fallot with associated left superior vena cava and coronary sinus atrial septal defect. The initial diagnosis was made by echocardiography. The patient underwent complete repair at 2 months of age. Her postoperative course was complicated by low cardiac output requiring ECMO. She was subsequently weaned off of ECMO and discharged home. She continues to do well on serial follow-up.
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Video 1 Modified high parasternal short axial sweep demonstrating LSVC draining directly into the LA, indicating an unroofed coronary sinus. LUPV is seen draining into the LA in the vicinity of the LSVC.
Supplementary material 1 (WMV 541 kb)
Video 2 Subcostal long axial sweep demonstrating a PFO and coronary sinus ASD with further posterior angulation.
Supplementary material 2 (WMV 1510 kb)
Video 3 Subcostal sagittal axial sweep demonstrating the IVC and SVC entering the RA.
Supplementary material 3 (WMV 971 kb)
Video 4 Subcostal right anterior oblique sweep demonstrating narrow RVOT, large VSD, and anterior displacement of the aorta.
Supplementary material 4 (WMV 768 kb)
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Mallula, K.K., Patel, N.D., Abdulla, Ri. et al. Tetralogy of Fallot with Left Superior Vena Cava and Coronary Sinus Atrial Septal Defect: A Rare Association. Pediatr Cardiol 36, 1100–1101 (2015). https://doi.org/10.1007/s00246-015-1137-1
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DOI: https://doi.org/10.1007/s00246-015-1137-1