Abstract
We describe the temporal bone computed tomography (CT) findings of an unusual case of branchio-oto-renal syndrome with ectopic ossicles that are partially located in the middle cranial fossa. We also describe quantitative temporal bone CT assessment pertaining to cochlear implantation in the setting of anomalous cochlear anatomy associated with this syndrome.
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Ginat, D.T., Ferro, L. & Gluth, M.B. Anatomic and Quantitative Temporal Bone CT for Preoperative Assessment of Branchio-Oto-Renal Syndrome. Clin Neuroradiol 26, 481–483 (2016). https://doi.org/10.1007/s00062-016-0502-7
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DOI: https://doi.org/10.1007/s00062-016-0502-7