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Polymyositis associated with primary biliary cirrhosis

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Summary

The coexistence of polymyositis (PM) and primary biliary cirrhosis (PBC) is rare; only nine cases have been described in English literature. We report a case of a 46-year- old woman presenting with these two autoimmune diseases. The diagnosis of PM was based on the symmertrical, proximal limb muscle weakness, elevated muscle enzymes and was confirmed with the electromyography and muscle biopsy. The diagnosis of PBC was based on the increased serum levels of alkaline phosphatase, gamma glutamyltransferase, IgM immunoglobulin, the presence of antimitochondrial antibodies and jdiagnostic liver biopsy.

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Boki, K.A., Dourakis, S.P. Polymyositis associated with primary biliary cirrhosis. Clin Rheumatol 14, 375–378 (1995). https://doi.org/10.1007/BF02208358

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