Activity of trabectidin in desmoplastic small round cell tumor
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- López-González, A., Cantos, B., Tejerina, E. et al. Med Oncol (2011) 28: 644. doi:10.1007/s12032-010-9687-9
Desmoplastic small round cell tumor (DSRCT) is a rare and aggressive cancer that typically arises in teenage boys. As a result of its low prevalence, there have been few studies of its treatment and impact on survival. Here, we report the case of a patient who was refractory to multiple drugs but remains stable with trabectedin. To our knowledge, this is the first published report that supports antitumoral activity of trabectedin in DSRCT.