Current Gastroenterology Reports

, Volume 13, Issue 2, pp 193–201

Biliary Disease in Children


DOI: 10.1007/s11894-010-0169-1

Cite this article as:
Goldman, M. & Pranikoff, T. Curr Gastroenterol Rep (2011) 13: 193. doi:10.1007/s11894-010-0169-1


Biliary diseases in children are infrequent; however, they can be associated with high morbidity and mortality if an accurate diagnosis is not made and adequate treatment provided in a timely fashion. Biliary atresia, choledochal cysts, gallbladder disease, and Alagille syndrome can be associated with similar clinical symptoms, laboratory findings, and radiographic findings, which makes accurate diagnosis difficult. The correct treatment for each of these clinical entities is different and can significantly reduce morbidity and mortality from these diseases. In this article, we discuss the epidemiology, approach to diagnosis, prognosis, and treatment modalities for these four disease processes.


Biliary atresiaCholedochal cystCholelithiasisBiliary dyskinesiaKasaiAlagille syndromeHyperbilirubinemiaHepatoportoenterostomyHepatic iminodiacetic acid scanMagnetic resonance cholangiopancreatographyCholecystectomyEndoscopic retrograde cholangiopancreatographyCholestasisLiver transplantation

Copyright information

© Springer Science+Business Media, LLC 2011

Authors and Affiliations

  1. 1.Department of Surgery, Section of Pediatric SurgeryWake Forest University School of MedicineWinston SalemUSA