The International Journal of Cardiovascular Imaging

, Volume 20, Issue 6, pp 517–522

Tropical endomyocardial fibrosis (Davies’ disease): case report demonstrating the role of magnetic resonance imaging

  • Jan P. Smedema
  • Stephan K. G. Winckels
  • Gabriel Snoep
  • Jindra Vainer
  • Sebastiaan C. A. M. Bekkers
  • Harry J. G. M. Crijins
Article

DOI: 10.1007/s10554-004-1095-9

Cite this article as:
Smedema, J.P., Winckels, S.K.G., Snoep, G. et al. Int J Cardiovasc Imaging (2004) 20: 517. doi:10.1007/s10554-004-1095-9

Abstract

Tropical endomyocardial fibrosis (TEMF), a restrictive cardiomyopathy of unclear etiology, is an endemic disease in equatorial Africa, South America and India. The patients are usually young, the onset of the disease and its clinical manifestations insidious, and the prognosis poor. We currently present a 50-year-old Congolese female who was referred with symptoms of progressive right-sided heart failure due to isolated TEMF of the right ventricle. Surgical resection of regional endomyocardial fibrosis was not possible and our patient was referred for cardiac transplantation. Cardiac magnetic resonance imaging (CMR) demonstrated the primary and secondary structural and functional abnormalities. CMR seems ideally suited to diagnose this condition and monitor response to medical and/or surgical therapy.

Keywords

cardiac magnetic resonance imaging restrictive cardiomyopathy tropical endomyocardial fibrosis 

Abbreviations

CMR

magnetic resonance imaging

RA

right atrium

RV

right ventricle

TEM

tropical endomyocardial fibrosis

Copyright information

© Kluwer Academic Publishers 2004

Authors and Affiliations

  • Jan P. Smedema
    • 1
  • Stephan K. G. Winckels
    • 1
  • Gabriel Snoep
    • 2
  • Jindra Vainer
    • 1
  • Sebastiaan C. A. M. Bekkers
    • 1
  • Harry J. G. M. Crijins
    • 1
  1. 1.Department of CardiologyMaastricht University HospitalMaastrichtThe Netherlands
  2. 2.Department of RadiologyMaastricht University HospitalThe Netherlands