Clinical Rheumatology

, Volume 26, Issue 8, pp 1359–1361

Pulmonary hypertension in a patient with adult-onset stills disease

  • Eisha Mubashir
  • M. Mubashir Ahmed
  • Samina Hayat
  • Maureen Heldmann
  • Seth Mark Berney
Case Report

DOI: 10.1007/s10067-006-0382-3

Cite this article as:
Mubashir, E., Ahmed, M.M., Hayat, S. et al. Clin Rheumatol (2007) 26: 1359. doi:10.1007/s10067-006-0382-3

Abstract

Pulmonary manifestations of adult-onset Still’s disease (AOSD) include aseptic pneumonitis, pleural effusions, rarely acute respiratory distress syndrome, and restrictive lung disease. Pulmonary arterial hypertension (PAH) occurs with several rheumatologic diseases, however, has only been reported once in AOSD. We describe a 29-year-old woman with a 9-year history of AOSD, who developed PAH without any other obvious cause. Therefore, we conclude that this is likely a result of pulmonary vascular changes related to AOSD.

Keywords

Adult-onset Still’s diseaseAutoimmune rheumatic diseasesPulmonary arterial hypertension

Copyright information

© Clinical Rheumatology 2006

Authors and Affiliations

  • Eisha Mubashir
    • 1
  • M. Mubashir Ahmed
    • 1
  • Samina Hayat
    • 1
  • Maureen Heldmann
    • 2
  • Seth Mark Berney
    • 1
  1. 1.Department of Medicine, Center of Exellence for Arthritis and RheumatologyLouisiana State University Health Science CenterShreveportUSA
  2. 2.Department of RadiologyLouisiana State University Health Science CenterShreveportUSA