Pediatric and Developmental Pathology

, Volume 2, Issue 1, pp 94–100

Ivemark's Renal-Hepatic-Pancreatic Dysplasia: Analytic Approach to a Perinatal Autopsy


  • Robert W.  Bendon
    • Department of Pathology, Kosair Children's Hospital, 231 E. Chestnut Street, Louisville, KY 40202, USA

DOI: 10.1007/s100249900096

Cite this article as:
Bendon, R. Pediatr. Dev. Pathol. (1999) 2: 94. doi:10.1007/s100249900096


A case of Ivemark's renal-hepatic dysplasia syndrome is presented. The findings are suggestive of a ductal obstructive process anatomically located at the junction of ducts with the parenchyma. The differential diagnosis includes Meckel syndrome, short rib polydactyly syndromes, and glutaric aciduria type 2. The molecular basis for this syndrome remains unknown.

Key words: kidney, liver, pancreas, dysplasia, glomerulocystic, Ivemark's syndrome

Copyright information

© Springer-Verlag New York Inc. 1999