Pediatric and Developmental Pathology

, Volume 8, Issue 6, pp 654–657

Zimmermann-Laband Syndrome in an Infant With an Atypical Histologic Finding

Authors

    • Department of Pediatrics, Section of Pediatric Endocrinology, School of MedicineSelcuk University
  • Ozgur Pirgon
    • Department of Pediatrics, Section of Pediatric Endocrinology, School of MedicineSelcuk University
  • Ahmet Sert
    • Department of Pediatrics, Section of Pediatric Endocrinology, School of MedicineSelcuk University
  • Hatice Toy
    • Department of Pathology, School of MedicineSelcuk University
Article

DOI: 10.1007/s10024-005-0048-1

Cite this article as:
Atabek, M.E., Pirgon, O., Sert, A. et al. Pediatr Dev Pathol (2005) 8: 654. doi:10.1007/s10024-005-0048-1

Abstract

Zimmermann-Laband syndrome is an inherited disorder that is characterized by abnormalities of the head, face, hands, and feet. Most children with this disorder have generalized hypertrichosis, large gingivae, and hypoplasia of the fingernails and toenails. We report a male infant who exhibited typical features of Zimmermann-Laband syndrome with an unusual histopathologic finding. Excised tissue from the infant’s gingivae showed papillary projections that were composed of hyperplastic stratified squamous epithelium with different amounts of keratinization.

Keywords

Zimmermann-Laband syndromehypertrichosisgingival hyperplasiainfant

Copyright information

© Society for Pediatric Pathology 2005