Article

Pediatric and Developmental Pathology

, Volume 8, Issue 6, pp 654-657

First online:

Zimmermann-Laband Syndrome in an Infant With an Atypical Histologic Finding

  • Mehmet Emre AtabekAffiliated withDepartment of Pediatrics, Section of Pediatric Endocrinology, School of Medicine, Selcuk University Email author 
  • , Ozgur PirgonAffiliated withDepartment of Pediatrics, Section of Pediatric Endocrinology, School of Medicine, Selcuk University
  • , Ahmet SertAffiliated withDepartment of Pediatrics, Section of Pediatric Endocrinology, School of Medicine, Selcuk University
  • , Hatice ToyAffiliated withDepartment of Pathology, School of Medicine, Selcuk University

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Abstract

Zimmermann-Laband syndrome is an inherited disorder that is characterized by abnormalities of the head, face, hands, and feet. Most children with this disorder have generalized hypertrichosis, large gingivae, and hypoplasia of the fingernails and toenails. We report a male infant who exhibited typical features of Zimmermann-Laband syndrome with an unusual histopathologic finding. Excised tissue from the infant’s gingivae showed papillary projections that were composed of hyperplastic stratified squamous epithelium with different amounts of keratinization.

Keywords

Zimmermann-Laband syndrome hypertrichosis gingival hyperplasia infant