CASE REPORT

Pediatric and Developmental Pathology

, Volume 8, Issue 1, pp 105-114

First online:

“Proximal-type” and Classic Epithelioid Sarcomas Represent a Clinicopathologic Continuum: Case Report

  • Dinesh RakhejaAffiliated withDepartment of Pathology, Children’s Medical Center of DallasDepartment of Pathology, University of Texas Southwestern Medical Center
  • , Kathleen S. WilsonAffiliated withDepartment of Pathology, University of Texas Southwestern Medical Center
  • , John MeehanAffiliated withDepartment of Radiology, Children’s Medical Center of Dallas
  • , Roger A. SchultzAffiliated withDepartment of Pathology, University of Texas Southwestern Medical Center
  • , Ana M. GomezAffiliated withDepartment of Pathology, Children’s Medical Center of DallasDepartment of Pathology, University of Texas Southwestern Medical Center Email author 

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Abstract

We report a case of an epithelioid sarcoma that occurred in the right hand of a 14−year-old boy and had the “proximal-type” morphology and a complex, near-tetraploid karyotype. The tumor metastasized to the lungs, where the morphology was typical for the classic epithelioid sarcoma. Based on the morphologic and cytogenetic findings in this case, we suggest that the proximal-type and the classic epithelioid sarcomas are not distinct entities but represent a continuum.

Keywords

epithelioid sarcoma proximal-type epithelioid sarcoma cytogenetics