Pediatric and Developmental Pathology

, Volume 8, Issue 1, pp 105–114

“Proximal-type” and Classic Epithelioid Sarcomas Represent a Clinicopathologic Continuum: Case Report

Authors

  • Dinesh Rakheja
    • Department of PathologyChildren’s Medical Center of Dallas
    • Department of PathologyUniversity of Texas Southwestern Medical Center
  • Kathleen S. Wilson
    • Department of PathologyUniversity of Texas Southwestern Medical Center
  • John Meehan
    • Department of RadiologyChildren’s Medical Center of Dallas
  • Roger A. Schultz
    • Department of PathologyUniversity of Texas Southwestern Medical Center
    • Department of PathologyChildren’s Medical Center of Dallas
    • Department of PathologyUniversity of Texas Southwestern Medical Center
CASE REPORT

DOI: 10.1007/s10024-004-7086-y

Cite this article as:
Rakheja, D., Wilson, K.S., Meehan, J. et al. Pediatr Dev Pathol (2005) 8: 105. doi:10.1007/s10024-004-7086-y

Abstract

We report a case of an epithelioid sarcoma that occurred in the right hand of a 14−year-old boy and had the “proximal-type” morphology and a complex, near-tetraploid karyotype. The tumor metastasized to the lungs, where the morphology was typical for the classic epithelioid sarcoma. Based on the morphologic and cytogenetic findings in this case, we suggest that the proximal-type and the classic epithelioid sarcomas are not distinct entities but represent a continuum.

Keywords

epithelioid sarcomaproximal-type epithelioid sarcomacytogenetics

Copyright information

© Society for Pediatric Pathology 2004