Pediatric Nephrology

, Volume 13, Issue 8, pp 678–682

Recurrent bacteremia with enteric pathogens in recessive polycystic kidney disease


  • C. E. Kashtan
    • Division of Pediatric Nephrology, Department of Pediatrics, University of Minnesota Medical School, Box 491, 515 Delaware Street, SE, Minneapolis, MN 55455, USA, Tel.: +1-612-626-2922, Fax: +1-612-626-2791
  • William A. Primack
    • Department of Pediatrics, Fallon Clinic, Auburn, Massachusetts, USA
  • G. Kainer
    • Division of Nephrology, Sydney Children’s Hospital, Sydney, Australia
  • Andrew R. Rosenberg
    • Division of Nephrology, Sydney Children’s Hospital, Sydney, Australia
  • Ruth A. McDonald
    • Division of Nephrology, Department of Pediatrics, Children’s Hospital, Seattle, Washington, USA
  • Bradley A. Warady
    • Section of Nephrology, Children’s Mercy Hospital, Kansas City, Missouri, USA
Original Article

DOI: 10.1007/s004670050680

Cite this article as:
Kashtan, C., Primack, W., Kainer, G. et al. Pediatr Nephrol (1999) 13: 678. doi:10.1007/s004670050680


Eight children with autosomal recessive polycystic kidney disease (ARPKD) and recurrent bacteremia with enteric pathogens are described. Typical clinical features of bacterial cholangitis were absent, although in five patients histological and/or microbiological data indicated that the bacteremic episodes originated in the biliary tree. Bacteremia with enteric pathogens or recurrent culture-negative febrile illness in a child with ARPKD should raise suspicion of cholangitis, even in the absence of typical clinical findings.

Key words Autosomal recessive polycystic kidney diseaseCongenital hepatic fibrosisCholangitisCaroli disease

Copyright information

© IPNA - International Pediatric Nephrology Association New York, USA 1999