A sporadic case of paraganglioma undetected by urine metabolite screening
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- Bockenhauer, D., Rees, L., Neumann, H. et al. Pediatr Nephrol (2008) 23: 1889. doi:10.1007/s00467-008-0841-y
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Phaeochromocytoma is a rare cause of hypertension in children, but important to be recognised, as hypertension can be severe and surgery is often curative. Here, we report on a 7-year-old boy with a phaeochromocytoma, who had normal levels of commonly assayed catecholamine metabolites in the urine. Postoperatively, the patient developed renal vein thrombosis. Appropriate screening tests for phaeochromocytomas, peri-operative management, and the high incidence of an underlying genetic basis, even in sporadic cases, are discussed.