Pediatric Surgery International

, Volume 29, Issue 8, pp 841–845

Hepatobiliary cystadenoma: a rare pediatric tumor

  • Sifrance Tran
  • Loren Berman
  • Nitin R. Wadhwani
  • Marybeth Browne
Case Report

DOI: 10.1007/s00383-013-3290-z

Cite this article as:
Tran, S., Berman, L., Wadhwani, N.R. et al. Pediatr Surg Int (2013) 29: 841. doi:10.1007/s00383-013-3290-z
  • 193 Downloads

Abstract

Hepatobiliary cystadenoma is a rare hepatic neoplasm that has been reported only 10 times in the pediatric population. Although considered a benign cystic tumor of the liver, hepatobiliary cystadenoma has a high risk of recurrence with incomplete excision and a potential risk for malignant degeneration. Complete tumor excision with negative margins is the mainstay in treatment. Unfortunately, due to the paucity of cases and its vague presentation, hepatobiliary cystadenoma is rarely diagnosed preoperatively. Therefore, in patients with hepatic cystic masses without a clear diagnosis, total resection of the lesion with negative margins is indicated to adequately evaluate for malignant potential and limit the risk of recurrence. We describe a 2-year-old girl with an asymptomatic abdominal mass that was found to be hepatobiliary cystadenoma. In addition, the pathogenic, histopathologic and clinical features of hepatobiliary cystadenoma are reviewed.

Keywords

Abdominal mass Liver cysts Hepatobiliary cystadenoma Pediatric Hepatic resection Hepatic mass 

Copyright information

© Springer-Verlag Berlin Heidelberg 2013

Authors and Affiliations

  • Sifrance Tran
    • 1
  • Loren Berman
    • 1
  • Nitin R. Wadhwani
    • 2
  • Marybeth Browne
    • 1
    • 3
  1. 1.Division of Pediatric SurgeryAnn and Robert H. Lurie Children’s Hospital of ChicagoChicagoUSA
  2. 2.Division of PathologyAnn and Robert H. Lurie Children’s Hospital of ChicagoChicagoUSA
  3. 3.Northwestern University Feinberg School of Medicine, Ann and Robert H. Lurie Children’s Hospital of ChicagoChicagoUSA

Personalised recommendations