Focus Session

Child's Nervous System

, Volume 20, Issue 5, pp 323-328

First online:

History, anatomic forms, and pathogenesis of Chiari I malformations

  • Edgardo SchijmanAffiliated withSection of Neurosurgery, Hospital C. DurandDivision of Neurosurgery, University of Buenos Aires School of Medicine Email author 

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Chiari I malformations constitute a group of entities of congenital or acquired etiology that have in common descent of the cerebellar tonsils into the cervical spinal canal. In recent years, since the advent of magnetic resonance imaging, an increasing number of asymptomatic, doubtfully symptomatic, and minimally symptomatic patients with Chiari I malformations have been diagnosed. This has resulted in controversy about the multiple therapeutic strategies indicated for these problems.


With the intention of updating the knowledge that we currently have on the Chiari I malformation and the related syringomyelia we review the literature and discuss the historical background, pathogenesis, anatomic forms, clinical presentation, and diagnostic procedures of these abnormalities.


Chiari I malformation Foramen magnum decompression Hydromyelia Posterior fossa decompression Syringomyelia