European Radiology

, Volume 12, Issue 1, pp 190–192

Endotracheal neurofibroma in neurofibromatosis type 1: an unusual manifestation

  • Jürgen K. Willmann
  • Dominik Weishaupt
  • Peter B. Kestenholz
  • Alexander von Smekal
  • Borut Marincek
Chest

DOI: 10.1007/s003300100892

Cite this article as:
Willmann, J.K., Weishaupt, D., Kestenholz, P.B. et al. Eur Radiol (2002) 12: 190. doi:10.1007/s003300100892

Abstract

Tracheal involvement is an extremely rare manifestation in patients with neurofibromatosis type 1 (NF-1). We present a 33-year-old women with NF-1 suffering from progressive dyspnea. Multislice spiral CT revealed a neurofibroma located within the trachea with intratracheal extension. To our knowledge, this is the first report of an intratracheal neurofibroma which has been documented by CT. This indicates that multislice spiral CT allows accurate demonstration of localization and extent of this rare manifestation of neurofibromas.

Neurofibroma NF-1 Neurofibromatosis Multislice spiral CT Trachea

Copyright information

© Springer-Verlag 2001

Authors and Affiliations

  • Jürgen K. Willmann
    • 1
  • Dominik Weishaupt
    • 1
  • Peter B. Kestenholz
    • 2
  • Alexander von Smekal
    • 1
  • Borut Marincek
    • 1
  1. 1.Institute of Diagnostic Radiology, University of Zurich, Rämistrasse 100, 8091 ZurichSwitzerland
  2. 2.Clinic of Pulmonary Surgery, University of Zurich, Rämistrasse 100, 8091 ZurichSwitzerland