Case Report

Skeletal Radiology

, Volume 39, Issue 6, pp 595-600

First online:

Primary cutaneous Ewing’s sarcoma/primitive neuroectodermal tumor manifesting numerous small and huge ulcerated masses: its complete remission by chemotherapy and magnetic resonance imaging findings

  • Won-Jong BahkAffiliated withDepartment of Orthopedic Surgery, Uijeongbu St. Mary’s Hospital, The Catholic University of Korea Email author 
  • , Eun-Deok ChangAffiliated withDepartment of Pathology, Uijeongbu St. Mary’s Hospital, The Catholic University of Korea
  • , Jung Min BaeAffiliated withDepartment of Dermatology, Uijeongbu St. Mary’s Hospital, The Catholic University of Korea
  • , Kyung-Ah ChunAffiliated withDepartment of Radiology, Uijeongbu St. Mary’s Hospital, The Catholic University of Korea
  • , An-Hee LeeAffiliated withDepartment of Pathology, Uijeongbu St. Mary’s Hospital, The Catholic University of Korea
  • , Sang-Young RhoAffiliated withDepartment of Hemato-oncology, Uijeongbu St. Mary’s Hospital, The Catholic University of Korea
  • , Jin Woo KimAffiliated withDepartment of Dermatology, Uijeongbu St. Mary’s Hospital, The Catholic University of Korea

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Abstract

Extraskeletal Ewing’s sarcoma (ES) and primitive neuroectodermal tumor (PNET) are widely regarded as clinically and histologically identical tumors which consist of small blue round cells. Extraskeletal ESs/PNETs usually occur in the deep soft tissues of the paraspinal region, chest wall, or lower extremities. However, superficially located cases, so-called cutaneous ESs/PNETs, are exceedingly rare, and the vast majority of the reported cases present as a single small mass. We present magnetic resonance imaging (MRI) findings and clinical course of a unique case of primary cutaneous ES/PNET presenting as numerous huge masses with severe ulceration on them.

Keywords

Primary cutaneous Ewing’s sarcoma/primitive neuroectodermal tumor MRI findings Multiple huge masses Clinical outcome