Primary cutaneous Ewing’s sarcoma/primitive neuroectodermal tumor manifesting numerous small and huge ulcerated masses: its complete remission by chemotherapy and magnetic resonance imaging findings
First Online: 12 February 2010 Received: 22 August 2009 Revised: 27 December 2009 Accepted: 28 December 2009 DOI:
Cite this article as: Bahk, W., Chang, E., Bae, J.M. et al. Skeletal Radiol (2010) 39: 595. doi:10.1007/s00256-009-0872-x Abstract
Extraskeletal Ewing’s sarcoma (ES) and primitive neuroectodermal tumor (PNET) are widely regarded as clinically and histologically identical tumors which consist of small blue round cells. Extraskeletal ESs/PNETs usually occur in the deep soft tissues of the paraspinal region, chest wall, or lower extremities. However, superficially located cases, so-called cutaneous ESs/PNETs, are exceedingly rare, and the vast majority of the reported cases present as a single small mass. We present magnetic resonance imaging (MRI) findings and clinical course of a unique case of primary cutaneous ES/PNET presenting as numerous huge masses with severe ulceration on them.
Keywords Primary cutaneous Ewing’s sarcoma/primitive neuroectodermal tumor MRI findings Multiple huge masses Clinical outcome References
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