Pediatric Radiology

, Volume 44, Issue 4, pp 479–483

Congenital peribronchial myofibroblastic tumor: prenatal imaging clues to differentiate from other fetal chest lesions

Authors

    • Department of Radiology, MLC 5031Cincinnati Children’s Hospital Medical Center
  • Foong-Yen Lim
    • Department of Pediatric Surgery and Fetal Care Center of CincinnatiCincinnati Children’s Hospital Medical Center
  • Jerzy Stanek
    • Department of PathologyCincinnati Children’s Hospital Medical Center
  • Constance Bitters
    • Department of Radiology, MLC 5031Cincinnati Children’s Hospital Medical Center
  • Beth M. Kline-Fath
    • Department of Radiology, MLC 5031Cincinnati Children’s Hospital Medical Center
Case Report

DOI: 10.1007/s00247-013-2817-8

Cite this article as:
Calvo-Garcia, M.A., Lim, F., Stanek, J. et al. Pediatr Radiol (2014) 44: 479. doi:10.1007/s00247-013-2817-8

Abstract

We present a prenatal case of congenital peribronchial myofibroblastic tumor referred as a congenital pulmonary airway malformation (CPAM) with hydrops and polyhydramnios at 30 weeks’ gestational age. US and fetal MRI findings did not fit with the referral diagnosis, raising the possibility of intrinsic lung tumor. Fetal hydrops worsened and the baby was successfully delivered by ex utero intrapartum treatment (EXIT) to resection at 31 weeks’ gestational age. To the best of our knowledge, this is a unique case of congenital peribronchial myofibroblastic tumor that underwent comprehensive prenatal evaluation and EXIT procedure with good outcome.

Keywords

Congenital peribronchial myofibroblastic tumor Lung Prenatal diagnosis Fetal MRI Sonography

Copyright information

© Springer-Verlag Berlin Heidelberg 2013