, Volume 38, Issue 8, p 916
Date: 06 May 2008

Pelvic plexiform neurofibroma involving the urinary bladder

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A 14-year-old girl diagnosed with neurofibromatosis type I presented with obstructive urinary symptoms. Ultrasonography and MRI of the abdomen and pelvis revealed extensive plexiform neurofibromas with involvement of the pelvic viscera, including the bladder.

Visceral neurofibromatosis with urinary bladder involvement is rare and presenting features include irritative voiding symptoms and hematuria due to recurrent urinary tract infections, enuresis, and urinary obstruction. On US (Fig. 1) neurofibromas appear as solid, round, or oval masses, and bladder involvement can manifest as a focal mass or diffuse bladder wall thickening. On MR imaging (Fig. 2), neurofibromas have homogeneous low-signal intensity on T1-W images and homogeneous high-signal intensity on T2-W images, along with a target sign, which is a more specific sign of a neurogenic tumor [1]. MR imaging is often performed after US, because MR provides greater detail and tissue characterization, as seen in these images. Differ ...