Pediatric Radiology

, Volume 36, Issue 6, pp 566–568

Congenital absence of the portal vein in a child with Turner syndrome

  • Jacob A. Noe
  • Heather C. Pittman
  • Edward M. Burton
Case Report

DOI: 10.1007/s00247-006-0169-3

Cite this article as:
Noe, J.A., Pittman, H.C. & Burton, E.M. Pediatr Radiol (2006) 36: 566. doi:10.1007/s00247-006-0169-3

Abstract

Congenital absence of the portal vein (CAPV) is a rare malformation associated with hepatic encephalopathy and liver function abnormalities. We report a case of a 2-year-old with Turner syndrome, CAPV, and congenital heart malformations.

Keywords

Portal vein absenceTurner syndromeHepatic malformation

Copyright information

© Springer-Verlag 2006

Authors and Affiliations

  • Jacob A. Noe
    • 1
  • Heather C. Pittman
    • 2
  • Edward M. Burton
    • 1
  1. 1.Department of Radiology, University of Tennessee College of Medicine–Chattanooga BranchErlanger Health SystemChattanoogaUSA
  2. 2.Department of Pediatrics, University of Tennessee College of Medicine–Chattanooga BranchErlanger Health SystemChattanoogaUSA