Pediatric Radiology

, Volume 35, Issue 4, pp 387–391

Imaging findings in pleuropulmonary blastoma

Original Article

DOI: 10.1007/s00247-004-1367-5

Cite this article as:
Naffaa, L.N. & Donnelly, L.F. Pediatr Radiol (2005) 35: 387. doi:10.1007/s00247-004-1367-5

Abstract

Background: Pleuropulmonary blastoma (PPB) is a rare tumor of the chest seen in young children and recently recognized as distinct from the pulmonary blastoma typically encountered in adults. Objective: The purpose of this study is to review and describe the findings of PPB on radiography and CT in four patients. Methods: Radiographs and CT findings were reviewed in four patients with pathologically proven PPB. Results: All four cases demonstrated large masses in the right hemithorax with heterogeneous low attenuation, pleural effusion, contralateral mediastinal shift, and lack of chest wall invasion. Conclusion: When a large pleural-based mass is identified in a young child, PPB should be considered. Suggestive findings include absence of chest wall invasion, presence of pleural fluid, right-sided location, and heterogeneous low attenuation.

Keywords

Pleuropulmonary blastomaThoracic tumorYoung childrenCT

Copyright information

© Springer-Verlag 2005

Authors and Affiliations

  1. 1.Department of RadiologyCincinnati Children’s Hospital Medical CenterCincinnatiUSA