Pediatric Cardiology

, Volume 33, Issue 4, pp 659–662

Angina Pectoris with Troponin Increase in Arrhythmogenic Right Ventricle Dysplasia: Case Article and Review of the Literature

  • Jonathan Wagner
  • Mark H. Cohen
  • Marnie O’Donnell
  • Linda B. Pauliks
Case Report

DOI: 10.1007/s00246-012-0174-2

Cite this article as:
Wagner, J., Cohen, M.H., O’Donnell, M. et al. Pediatr Cardiol (2012) 33: 659. doi:10.1007/s00246-012-0174-2

Abstract

A 16-year-old Hispanic girl with arrhythmogenic right-ventricle dysplasia (ARVD) presented with angina pectoris and troponin increase on three occasions. There was a family history of sudden cardiac death in a cousin. Her mother was diagnosed with ARVD. The patient herself had a history of nonsustained ventricular tachycardia but did not meet diagnostic criteria for ARVD. Cardiac workup, including serial transthoracic echocardiograms and a coronary angiogram, showed a structurally normal heart without coronary artery stenosis. Results of cardiac magnetic resonance imaging were questionable, but endomyocardial biopsy did not show evidence of viral myocarditis by polymerase chain reaction. Genetic testing confirmed ARVD.

Keywords

Arrhythmogenic right-ventricle dysplasiaAngina pectorisCardiomyopathyTroponin

Copyright information

© Springer Science+Business Media, LLC 2012

Authors and Affiliations

  • Jonathan Wagner
    • 1
  • Mark H. Cohen
    • 1
  • Marnie O’Donnell
    • 1
  • Linda B. Pauliks
    • 1
  1. 1.Division of Pediatric CardiologyPenn State Hershey Medical CollegeHersheyUSA