Pediatric Cardiology

, Volume 29, Issue 4, pp 800–803

The Challenge of Diagnosing Arrhythmogenic Right Ventricular Cardiomyopathy in the Young

Case Report

DOI: 10.1007/s00246-008-9238-8

Cite this article as:
Sanatani, S., Duncan, W. & Chan, S. Pediatr Cardiol (2008) 29: 800. doi:10.1007/s00246-008-9238-8


We report two cases of arrhythmogenic right ventricular cardiomyopathy (ARVC) in the pediatric age group. In both cases, the diagnosis was considered and pursued but would not be made utilizing Task Force Criteria. The diagnosis was made based on the morphology of a single beat during exercise testing. We illustrate the difficulty of diagnosing ARVC in the young even with a heightened index of suspicion.


Arrhythmogenic right ventricular cardiomyopathySudden deathPediatrics

Copyright information

© Springer Science+Business Media, LLC 2008

Authors and Affiliations

  • Shubhayan Sanatani
    • 1
    • 2
  • Walter Duncan
    • 1
  • Suzanne Chan
    • 3
  1. 1.Division of Pediatric Cardiology, Department of PediatricsUniversity of British Columbia, British Columbia Children’s HospitalVancouverCanada
  2. 2.Cardiac Pacing and ElectrophysiologyChildren’s Heart Centre, 1F9, British Columbia’s Children’s HospitalVancouverCanada
  3. 3.Department of Pathology and Laboratory MedicineUniversity of British Columbia, and Children’s and Women’s Health Centre of British ColumbiaVancouverCanada