Pediatric Cardiology

, Volume 29, Issue 1, pp 146–149

Pentalogy of Cantrell

Successful Early Correction
  • A. M. H. Korver
  • F. Haas
  • M. W. Freund
  • J. L. M. Strengers
Case Report

DOI: 10.1007/s00246-007-9032-z

Cite this article as:
Korver, A.M.H., Haas, F., Freund, M.W. et al. Pediatr Cardiol (2008) 29: 146. doi:10.1007/s00246-007-9032-z

Abstract

The pentalogy of Cantrell is a rare midline developmental field complex often with a dismal outcome. We present a newborn qualifying for Cantrell’s pentalogy with an abdominal wall defect, a diaphragmatic defect and a heart defect, a ventricular septal defect (VSD) and a left ventricular diverticulum. Early operative correction following accurate diagnostic work-up was prompted at the age of 11 weeks because of progressive heart failure. Beside correction of the VSD and the abdominal and diaphragmatic defects, resection of the distal part of the diverticulum was possible without damage to the LAD and preserving good contractility. Two years postoperative follow-up is uneventful.

Keywords

Pentalogy of CantrellMidline developmental fieldsVentricular diverticulum

Copyright information

© Springer Science+Business Media, LLC 2007

Authors and Affiliations

  • A. M. H. Korver
    • 1
  • F. Haas
    • 1
  • M. W. Freund
    • 1
  • J. L. M. Strengers
    • 1
  1. 1.Department of Pediatric CardiologyWilhelmina Children’s Hospital, University Medical Centre UtrechtUtrechtThe Netherlands