The Indian Journal of Pediatrics

, Volume 50, Issue 6, pp 679–683

Congenital ichthyosiform erythroderma and harlequin ichthyosis

Authors

  • P. Madhavachandran Nair
    • Department of Pediatrics and PathologyMedical College
  • K. Sabarinath
    • Department of Pediatrics and PathologyMedical College
  • V. G. Chellam
    • Department of Pediatrics and PathologyMedical College
Clinical Briefs

DOI: 10.1007/BF02957739

Cite this article as:
Nair, P.M., Sabarinath, K. & Chellam, V.G. Indian J Pediat (1983) 50: 679. doi:10.1007/BF02957739

Abstract

Five cases of congenital ichthyosiform erythroderma are being reported of these three were harleauin babies and two were collodion babies. The harlequin ichthyosis is a rare and dramatic manifestation of severe congenital ichthyosis, the longest reported suruival being 6 wk. The life span of our third case was unsually long, probably because of the intensive care received during the initial weeks. The clinical ana autopsy findings and the recent biochemical aspects are reviewed.

Key words

Congenital ichthyostform erythroderma harlequin fetus

Copyright information

© Dr. K C Chaudhuri Foundation 1983