European Journal of Pediatrics

, Volume 151, Issue 1, pp 73–75

Abnormal length of cilia—a cause of primary ciliary dyskinesia—a case report

  • B. Niggemann
  • A. Müller
  • Anke Nolte
  • N. Schnoy
  • U. Wahn
Pneumology

DOI: 10.1007/BF02073899

Cite this article as:
Niggemann, B., Müller, A., Nolte, A. et al. Eur J Pediatr (1992) 151: 73. doi:10.1007/BF02073899

Abstract

A 7-year-old Turkish boy had suffered from chronic coughing from early childhood. Severe bronchiectasis in the right lung was confirmed by bronchography. Ciliary beat frequency determined in a bronchial mucosal biopsy was markedly decreased (5.7 Hz). Electron microscopy revealed cilia with a length of 15 μm. No structural abnormality was found. A possible link between the abnormally long, slow beating cilia and the clinical symptoms is discussed.

Key words

Cilia Primary ciliary dyskinesia Mucociliary clearance 

Abbreviation

PCD

primary ciliary dyskinesia

Copyright information

© Springer-Verlag 1992

Authors and Affiliations

  • B. Niggemann
    • 1
  • A. Müller
    • 1
  • Anke Nolte
    • 1
  • N. Schnoy
    • 2
  • U. Wahn
    • 1
  1. 1.Department Paediatric Pneumology and ImmunologyUniversity Childrens Hospital (KAVH)Berlin 19Federal Republic of Germany
  2. 2.Institut PathologyFree University BerlinBerlinFederal Republic of Germany