Abnormal length of cilia—a cause of primary ciliary dyskinesia—a case report
- Cite this article as:
- Niggemann, B., Müller, A., Nolte, A. et al. Eur J Pediatr (1992) 151: 73. doi:10.1007/BF02073899
- 41 Downloads
A 7-year-old Turkish boy had suffered from chronic coughing from early childhood. Severe bronchiectasis in the right lung was confirmed by bronchography. Ciliary beat frequency determined in a bronchial mucosal biopsy was markedly decreased (5.7 Hz). Electron microscopy revealed cilia with a length of 15 μm. No structural abnormality was found. A possible link between the abnormally long, slow beating cilia and the clinical symptoms is discussed.
Key wordsCilia Primary ciliary dyskinesia Mucociliary clearance
primary ciliary dyskinesia