European Journal of Pediatrics

, Volume 151, Issue 8, pp 577–580

Atypical kawasaki disease: An often missed diagnosis

  • K. Boven
  • E. R. De Graeff-Meeder
  • W. Spliet
  • W. Kuis
Immunology/Allergology

DOI: 10.1007/BF01957725

Cite this article as:
Boven, K., De Graeff-Meeder, E.R., Spliet, W. et al. Eur J Pediatr (1992) 151: 577. doi:10.1007/BF01957725

Abstract

We describe four patients with vasculitis of the coronary and other medium sized arteries. Three of them died as a consequence of cardiac failure and the fourth had a ruptured aneurysm of the left common iliac artery. Coronary vasculitis is pathognomonic for Kawasaki disease (KD), but our patients had few other signs of this disorder, suggesting so called atypical KD. Because the described patients lacked most of the clinical criteria, the diagnosis was delayed. We focus on other clinical features in these patients and stress the importance of early recognition and treatment.

Key words

Atupical Kawasaki diseaseCoronary vasculitis

Abbreviations

AKD

atypical Kawasaki disease

KD

Kawasaki disease

Copyright information

© Springer-Verlag 1992

Authors and Affiliations

  • K. Boven
    • 1
  • E. R. De Graeff-Meeder
    • 1
  • W. Spliet
    • 2
  • W. Kuis
    • 1
  1. 1.Department of Immunology and RheumatologyUniversity Hospital for Children and YouthUtrechtThe Netherlands
  2. 2.Department of PathologyUniversity HosptialUtrechtThe Netherlands