Short Reports

Pediatric Radiology

, Volume 11, Issue 1, pp 42-45

First online:

Infantile hepatic hemangioendothelioma with subsequent malignant degeneration

  • S. G. KirchnerAffiliated withDepartment of Radiology and Radiological Sciences, Vanderbilt University Medical Center
  • , R. M. HellerAffiliated withDepartment of Radiology and Radiological Sciences, Vanderbilt University Medical Center
  • , A. G. KasselbergAffiliated withDepartment of Pathology, Vanderbilt University Medical Center
  • , H. L. GreeneAffiliated withDepartment of Pediatrics, Vanderbilt University Medical Center

Rent the article at a discount

Rent now

* Final gross prices may vary according to local VAT.

Get Access

Abstract

A 4 year old child was seen because of an enlarging epigastric mass and a rapidly falling hematocrit 31/2 years following steroid treatment for multiple hepatic hemangioendotheliomas. Technetium 99 m sulfur colloid liver scan and hepatic angiography confirmed the presence of a large, vascular mass involving the left lobe of the liver. A left hepatic lobectomy was performed and histopathology showed angiosarcoma. As children with hemangioendotheliomas of the liver begin to survive for longer periods of time, surveillance for the possible development of neoplastic disease is recommended.

Key words

Hemangioendothelioma, hepatic Hemangioendothelioma, malignant degeneration Angiosarcoma, hepatic Neoplasm, hepatic