Journal of Clinical Immunology

, Volume 2, Issue 2, pp 86–92

Primary immunodeficiency disorders in Sweden: Cases among children, 1974–1979

  • Anders Fasth
Original Articles

DOI: 10.1007/BF00916891

Cite this article as:
Fasth, A. J Clin Immunol (1982) 2: 86. doi:10.1007/BF00916891


A nationwide survey of symptomatic primary immunodeficiency disorders in children in Sweden during the 6-year period 1974–1979 resulted in 201 reported cases. The reported data for 174 children were analyzed. Antibody deficiencies were the most frequent (45.0%), followed by phagocytic disorders (22.0%) and combined T- and B-cell disorders (20.8%). Thirty-two children (18.4%) died, with the highest mortality for combined T- and B-cell defects. The sex ratio for all disorders was 2:1 for boys:girls. Neutropenia was significantly more common in the northern part of Sweden.

Key words

Primary immunodeficiencySwedish surveyfamilial incidenceinfections

Copyright information

© Plenum Publishing Corporation 1982

Authors and Affiliations

  • Anders Fasth
    • 1
  1. 1.Departments of Pediatrics and Clinical Immunology, Institute of Medical MicrobiologyUniversity of GöteborgGöteborgSweden
  2. 2.Department of PediatricsÖstra sjukhusetGöteborgSweden