Journal of Inherited Metabolic Disease

, Volume 18, Issue 2, pp 127–130

Nutritional value of essential amino acids in the treatment of adults with phenylketonuria

  • H. Dotremont
  • B. François
  • M. Diels
  • P. Gillis
Short Communication

DOI: 10.1007/BF00711746

Cite this article as:
Dotremont, H., François, B., Diels, M. et al. J Inherit Metab Dis (1995) 18: 127. doi:10.1007/BF00711746

Conclusion

The present short-term N-balance study in adult PKU patients receiving a mixture of LNAA establishes a limited retention of nitrogen. Whether lysine could be the limiting amino acid remains to be determined by new short-term N-balance studies, with lysine added to the LNAA mixture. Therefore, special caution should be taken in the long-term use in PKU patients of LNAA without any added lysine.

Copyright information

© Society for the Study of Inborn Errors of Metabolism and Kluwer Academic Publishers 1995

Authors and Affiliations

  • H. Dotremont
    • 1
    • 3
  • B. François
    • 1
    • 2
  • M. Diels
    • 1
  • P. Gillis
    • 3
  1. 1.Dr L. Willems InstituutUniversitaire CampusDiepenbeekBelgium
  2. 2.The Limburg University CentreDiepenbeekBelgium
  3. 3.Department of PediatricsVirga Jesse HospitalHasseltBelgium