Nutritional value of essential amino acids in the treatment of adults with phenylketonuria
- Cite this article as:
- Dotremont, H., François, B., Diels, M. et al. J Inherit Metab Dis (1995) 18: 127. doi:10.1007/BF00711746
The present short-term N-balance study in adult PKU patients receiving a mixture of LNAA establishes a limited retention of nitrogen. Whether lysine could be the limiting amino acid remains to be determined by new short-term N-balance studies, with lysine added to the LNAA mixture. Therefore, special caution should be taken in the long-term use in PKU patients of LNAA without any added lysine.