Interventional Neuroradiology

Neuroradiology

, Volume 38, Issue 6, pp 595-597

Ehlers-Danlos syndrome with a spontaneous caroticocavernous fistula occluded by detachable balloon: case report and review of literature

  • P. ForlodouAffiliated withService de Neuroradiologie, Hôpital G & R Laënnec
  • , A. de Kersaint-GillyAffiliated withService de Neuroradiologie, Hôpital G & R Laënnec
  • , J. PizzanelliAffiliated withService de Neuroradiologie, Hôpital G & R Laënnec
  • , M. P. ViarougeAffiliated withService de Neuroradiologie, Hôpital G & R Laënnec
  • , E. Auffray-CalvierAffiliated withService de Neuroradiologie, Hôpital G & R Laënnec

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Abstract

We report a caroticocavernous fistula (CCF) treated by an endovascular procedure in a young woman with Ehlers-Danlos syndrome type IV, with severe bilateral carotid and vertebral artery dysplasia. The CCF, which appeared after minor trauma, was successfully occluded by a detachable balloon introduced into the venous side by an arterial approach. Six previously published cases are reviewed, five successfully treated. The difficulties and risks of the endovascular procedure due to the vascular changes, are emphasised. The possibility of the venous approach is discussed.

Key words

Ehlers-Danlos syndrome Caroticocavernous fistula Endovascular procedure