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Primary extraosseous intradural spinal Ewing’s sarcoma: report of two cases

  • Case Report - Spine
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Abstract

Two cases of primary extraosseous intradural spinal Ewing’s sarcoma are reported with a review of the current literature. This rare neoplasm shares features with cerebral primitive neuroectodermal tumors, complicating a correct diagnosis. Gross total resection seems to be the main treatment, although adjuvant therapies could improve the prognosis. In case 1, a 56-year-old man presented with cauda equina syndrome. MRI showed an intradural tumor from L4 to S2. An emergency laminectomy was performed with gross total resection of a hemorrhagic tumor, followed by adjuvant treatment. In the second case, a 25-year-old female developed leg and lumbar pain. MRI study identified a homogeneously enhancing intradural mass at the L2-L3 level. A laminoplasty was performed, followed by tumor resection; no adjuvant treatment was administered afterwards. Immunohistochemical workup confirmed the diagnosis of Ewing’s sarcoma in both cases.

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Authors and Affiliations

  1. Department of Neurological Surgery, Hospital Universitario La Fe, Área Administrativa 5E, c/Bulevar Sur, s/n, 46026, Valencia, Spain

    Giovanni Pancucci, Juan Antonio Simal-Julian, Estela Plaza-Ramirez & Carlos Botella-Asunción

  2. Department of Radiology, Hospital Universitario La Fe, Valencia, Spain

    Raul García-Marcos

  3. Department of Pathology, Hospital Universitario La Fe, Valencia, Spain

    Empar Mayordomo-Aranda

Authors
  1. Giovanni Pancucci
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  2. Juan Antonio Simal-Julian
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  3. Estela Plaza-Ramirez
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  4. Raul García-Marcos
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  5. Empar Mayordomo-Aranda
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  6. Carlos Botella-Asunción
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Correspondence to Giovanni Pancucci.

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Pancucci, G., Simal-Julian, J.A., Plaza-Ramirez, E. et al. Primary extraosseous intradural spinal Ewing’s sarcoma: report of two cases. Acta Neurochir 155, 1229–1234 (2013). https://doi.org/10.1007/s00701-013-1739-4

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  • DOI: https://doi.org/10.1007/s00701-013-1739-4

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