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An endolymphatic sac tumor with imaging features of aneurysmal bone cysts: differential diagnostic considerations

  • Case Report
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Abstract

Background

Endolymphatic sac tumors (ELSTs) are rare, slow-growing tumors of the petrous bone. Despite the typical localisation, their radiological diagnosis can be challenging due to the variety of other tumors potentially showing similar features.

Case report

We present a 16-year-old child with progressive hearing loss, vertigo, and tinnitus who had a large petrous bone lesion showing imaging features of both ELSTs and aneurysmal bone cysts (ABCs). The patient underwent preoperative embolization of the tumor-supplying vessels and subsequently a subtotal resection. Histological examination revealed an ELST.

Conclusion

Despite the rarity of petrous bone ABCs, they should be considered as a differential diagnostic alternative of ELSTs due to their similar imaging appearance.

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Acknowledgments

The authors sincerely thank Prof. Andreas Rosenwald and Prof. Justus Müller for the histopathological evaluation of the tumor specimens. Furthermore, we thank Dr. The Vinh Nguyen, Prof. Cordula Matthies, Dr. Tilmann Schweitzer, and Dr. Rupert Wößner for the excellent clinical care of the presented patient.

Funding

No funding or other support was required for this study.

Conflict of interest

There are no relevant conflicts of interest to disclose.

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Authors and Affiliations

  1. Department of Neuroradiology, Universitätsklinikum Würzburg, Josef-Schneider-Strasse 11, 97080, Würzburg, Germany

    Bálint Alkonyi, Thomas Günthner-Lengsfeld, Johannes Nowak & László Solymosi

  2. Department of Otorhinolaryngology, Universitätsklinikum Würzburg, Würzburg, Germany

    Kristen Rak & Rudolf Hagen

Authors
  1. Bálint Alkonyi
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  2. Thomas Günthner-Lengsfeld
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  3. Kristen Rak
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Correspondence to Bálint Alkonyi.

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Alkonyi, B., Günthner-Lengsfeld, T., Rak, K. et al. An endolymphatic sac tumor with imaging features of aneurysmal bone cysts: differential diagnostic considerations. Childs Nerv Syst 30, 1583–1588 (2014). https://doi.org/10.1007/s00381-014-2453-0

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  • DOI: https://doi.org/10.1007/s00381-014-2453-0

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