Abstract
Hypoplastic left heart syndrome (HLHS) is a severe congenital heart defect that results in death if not treated shortly after birth. In approximately 60 to 70% of cases, HLHS can be detected prenatally and generally is well tolerated due to the presence of the foramen ovale and ductus arteriosus, which allow for blood to bypass the left side of the heart but still provide adequate blood flow to the systemic circulation. A rare case of HLHS involving a fetus with tricuspid valve stenosis, abnormal venous Doppler findings, and hydrops is reported.
References
Hinton RB Jr, Martin LJ, Tabangin ME, Mazwi ML, Cripe LH, Benson DW (2007) Hypoplastic left heart syndrome is heritable. J Am Coll Cardiol 50:1590–1595
Stamm C, Anderson RH, Ho SY (1997) The morphologically tricuspid valve in hypoplastic left heart syndrome. Eur J Cardiothorac Surg 12:587–592
Galindo A, Nieto O, Villagra S, Graneras A, Herraiz I, Mendoza A (2009) Hypoplastic left heart syndrome diagnosed in fetal life: associated findings, pregnancy outcome, and results of palliative surgery. Ultrasound Obstet Gynecol 33:560–566
Allen RH, Benson CB, Haug LW (2005) Pregnancy outcome of fetuses with a diagnosis of hypoplastic left ventricle on prenatal sonography. J Ultrasound Med 24:1199–1203
Huhta JC (2004) Guidelines for the evaluation of heart failure in the fetus with or without hydrops. Pediatr Cardiol 25:274–286
Gest AL, Martin CG, Moise AA, Hansen TN (1990) Reversal of venous blood flow with atrial tachycardia and hydrops in fetal sheep. Pediatr Res 28:223–226
Author information
Authors and Affiliations
Corresponding author
Rights and permissions
About this article
Cite this article
Divanović, A., Witte, D. & Michelfelder, E. A Fetus With Hypoplastic Left Heart Syndrome and Tricuspid Stenosis With Evolving Hydrops Fetalis. Pediatr Cardiol 33, 1210–1212 (2012). https://doi.org/10.1007/s00246-012-0253-4
Received:
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s00246-012-0253-4