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Kinder und Jugendliche mit Störungen der Geschlechtsentwicklung

Psychosexuelle und -soziale Entwicklung und Herausforderungen bei der Versorgung

Children and adolescents with disorders of sexual development

Psychosexual and social development and challenges for health care services

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Monatsschrift Kinderheilkunde Zeitschrift für Kinder- und Jugendmedizin Aims and scope Submit manuscript

Zusammenfassung

Die Diagnose von Störungen der Geschlechtsentwicklung (DSD) ist zu jedem Zeitpunkt im Leben eines Menschen möglich. Sie wirft eine Vielzahl von Fragen hinsichtlich der weiteren körperlichen, psychosexuellen und -sozialen Entwicklungen auf. Bisherige Erkenntnisse geben Hinweis darauf, dass ein weitestgehend störungsfreies Heranwachsen der betroffenen Kinder und Jugendlichen weniger von der Art und der Ausprägung der Störung selbst als vielmehr von der Art des Versorgungsmanagements abhängt. Für eine adäquate Versorgung von Personen mit DSD wird heute die Betreuung durch ein multiprofessionelles Team innerhalb eines spezialisierten Referenzzentrums als notwendig angesehen.

Abstract

Disorders of sexual development (DSD) may be diagnosed at any age. At the time of diagnosis, many questions concerning the individual’s physical, psychosexual, and psychosocial development emerge. There is evidence that developmental outcomes of DSD in children and adolescents depend less on the nature and severity of the disorder itself and more on the quality of the management. Only multiprofessional teams working in specialized centers may be able to guarantee adequate treatment for individuals with DSD.

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  1. Klinik für Kinder- und Jugendmedizin, Universitätsklinikum Schleswig-Holstein, Campus Lübeck, Ratzeburger Allee 160, 23538 , Lübeck, Deutschland

    M. Jürgensen, O. Hiort &  U. Thyen

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  1. M. Jürgensen
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  2. O. Hiort
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  3. U. Thyen
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Correspondence to U. Thyen.

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Jürgensen, M., Hiort, O. & Thyen, U. Kinder und Jugendliche mit Störungen der Geschlechtsentwicklung. Monatsschr Kinderheilkd 156, 226–233 (2008). https://doi.org/10.1007/s00112-008-1674-2

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  • DOI: https://doi.org/10.1007/s00112-008-1674-2

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