Abstract
Purpose
To review the imaging characteristics and evaluate the diagnostic value of echocardiography for diagnosing anomalous origin of the right coronary artery from the pulmonary artery (ARCAPA).
Methods
We retrospectively reviewed the echocardiographic records and compared these images with operative findings in six children with ARCAPA.
Results
ARCAPA was characterized by dilation of the left coronary artery, inappropriate origin of the right coronary artery from the pulmonary artery, and collaterals within the interventricular septum. The associated malformations included atrial septal defect in four cases. Four of six cases were diagnosed correctly, while the remaining two cases were misdiagnosed: one of fistula between the pulmonary artery and the left coronary artery and another of ARCAPA diagnosed intraoperatively in one case of atrial septal defect.
Conclusion
ARCAPA can be diagnosed by echocardiography but is prone to misdiagnosis. This malformation should be distinguished from coronary artery fistula.
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All procedures followed were in accordance with the ethical standards of the responsible committee on human experimentation (institutional and national) and with the Helsinki Declaration of 1975, as revised in 2008. This study was approved by Shanghai Children’s Medical Center, Shanghai Jiaotong University School of Medicine. Informed consent was obtained from all patients included in the study.
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Wu, LP., Zhang, YQ., Chen, LJ. et al. Diagnosis of anomalous origin of the right coronary artery from the pulmonary artery by echocardiography. J Med Ultrasonics 46, 335–341 (2019). https://doi.org/10.1007/s10396-019-00933-7
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DOI: https://doi.org/10.1007/s10396-019-00933-7