Abstract
Juvenile xanthogranuloma (JXG) is a benign, self-limiting histiocytic disorder of infancy and early childhood, usually presented as a single or multiple cutaneous lesions. The central nervous system is rarely affected by JXG. There were only a few reports of intracranial JXG cases which described its features on MR spectroscopy (MRS) and diffusion-weighted imaging (DWI), but its features on susceptibility-weighted imaging (SWI) and perfusion-weighted imaging (PWI) have not been reported yet. Here, we reported an intracranial JXG case which underwent multimodal MRI examinations including DWI, SWI, and PWI. The multimodal MRI provided a thorough insight into this disease and we found that intense enhancement and high perfusion may be important clues for the diagnosis.
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Su, J., Chen, N., Yue, Q. et al. Multimodel MRI features of an intracranial juvenile Xanthogranuloma. Childs Nerv Syst 35, 871–874 (2019). https://doi.org/10.1007/s00381-019-04102-6
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DOI: https://doi.org/10.1007/s00381-019-04102-6