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Cerebellopontine angle medulloblastoma with extensive nodularity in a child: case report and review of the literature

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Abstract

Background

Cerebellar medulloblastomas (MBs) are one of the most common posterior fossa tumors in children but rarely occur in the cerebellopontine angle (CPA). Only 39 cases of CPA MBs were reported in the literature, and most of them were classic and desmoplastic MBs.

Case presentation

A 22-month-old girl presented with progressive cerebellar ataxia. Magnetic resonance imaging showed a large tumor in the right CPA and obstructive hydrocephalus. Surgical resection was performed and achieved total tumor removal. Microscopic examination and immunohistochemical staining revealed the diagnosis of MB with extensive nodularity. The patient recovered from her symptoms during follow-up and was transferred for adjuvant chemotherapy.

Conclusion

MB should be considered as a differential diagnosis of a lesion in the CPA. The treatment and outcome of CPA MBs are similar to cerebellar MBs.

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Authors and Affiliations

  1. Division of Neurosurgery, Department of Surgery, Thammasat University Hospital, Faculty of Medicine, Thammasat University, 95 Klongneung, Khlong Luang, Pathum Thani, 12120, Thailand

    Raywat Noiphithak & Vich Yindeedej

  2. Department of Pathology and Forensic Medicine, Faculty of Medicine, Thammasat University, Khlong Luang, Pathum Thani, Thailand

    Chatchai Thamwongskul

Authors
  1. Raywat Noiphithak
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  2. Vich Yindeedej
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  3. Chatchai Thamwongskul
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Correspondence to Raywat Noiphithak.

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The authors did not receive any specific grant from funding agencies in the public, commercial, or not-for-specific sectors.

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Noiphithak, R., Yindeedej, V. & Thamwongskul, C. Cerebellopontine angle medulloblastoma with extensive nodularity in a child: case report and review of the literature. Childs Nerv Syst 33, 839–842 (2017). https://doi.org/10.1007/s00381-016-3325-6

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  • DOI: https://doi.org/10.1007/s00381-016-3325-6

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