Abstract
Malignant triton tumor is a malignant schwannoma with rhabdomyoblastic differentiation. This tumor is very rare. Case reports and small series have been reported in medical literature. Malignant triton tumor occurs predominantly in the trunk, head, neck, and lower extremities. There is an important relationship with Von Recklinghausen disease. Patients with this tumor have a very poor prognosis, with a rapid and fatal course. We present a clinical case with a giant malignant triton tumor of the scalp.
Level of Evidence: Level V, diagnostic study.
Similar content being viewed by others
References
Mijović Z, Mihailović D, Zivković N, Kostov M, Zivković S, Stojanović N (2013) A rare case of retroperitoneal malignant Triton tumor invading renal vein and small intestine. Vojnosanit Pregl 70(3):322–325
Locatelli P. Formation de membres surnumeraires. C R Assoc des Anatomistes. 20th meeting. Turín 1925.
Kamran SC, Howard SA, Shinagare AB, Krajewski KM, Jagannathan JP, Hornick JL, Ramaiya NH (2013) Malignant peripheral nerve sheath tumors: prognostic impact of rhabdomyoblastic differentiation (malignant triton tumors), neurofibromatosis 1 status and location. Eur J Surg Oncol 39(1):46–52
McConnell YJ, Giacomantonio CA (2012) Malignant triton tumors—complete surgical resection and adjuvant radiotherapy associated with improved survival. J Surg Oncol 106((1):51–56
Jaing TH, Chuang CC, Jung SM, Wu CT, Tseng CK, Chen CS (2013) Malignant triton tumor of cervical spine: report of one case and review of the literature. Pediatr Neonatol S1875-9572(13):00014–4
Li Z, Xiang J, Yan S, Gao F, Zheng S (2012) Malignant triton tumor of the retroperitoneum: a case report and review of the literature. World J Surg Oncol 10:96, Review
Kitamura Y, Abe K, Baba S, Isoda T, Maruoka Y, Matsuo Y, Kubo Y, Sakamoto A, Nishimura H, Sasaki M, Honda H (2013) Malignant triton tumor in the abdominal wall: a case report. Adv J Mol Imaging 3:9–13
Stasik CJ, Tawfik O (2006) Malignant peripheral nerve sheath tumor with rhabdomyosarcomatous differentiation (malignant triton tumor). Arch Pathol Lab Med 130(12):1878–1881, Review
Thoennissen NH, Schliemann C, Brunnberg U, Schmidt E, Staebler A, Stegger L, Bremer C, Schleicher C, Mesters RM, Müller-Tidow C, Berdel WE (2007) Chemotherapy in metastatic malignant triton tumor: report on two cases. Oncol Rep 18(4):763–767
Ethical standards
The manuscript does not contain clinical studies or patient data, and the publication of this case report has been approved by Hospital Ethics Committee.
Conflict of interest
None
Patient consent
Patients provided written consent for the use of their images.
Author information
Authors and Affiliations
Corresponding author
Rights and permissions
About this article
Cite this article
Pérez-Espadero, A., Nafs, F.J.E. & Troyas, R.G. Giant malignant triton tumor of the scalp. Eur J Plast Surg 38, 61–64 (2015). https://doi.org/10.1007/s00238-014-1023-8
Received:
Accepted:
Published:
Issue Date:
DOI: https://doi.org/10.1007/s00238-014-1023-8