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Dyschondrosteosis (Léri-Weill Syndrome) observed in a VIth century skeleton

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Abstract

Study of a case of dyschondrosteosis (Léri-Weill syndrome) was detected in a sixth-century adult skeleton.

In addition to the typical characteristics of dyschondrosteosis (shortness of the forearms and lower legs accompanied by Madelung's deformity of the radius), examination of the skeleton revealed bilateral acetabular dysplasia.

No degenerative change (osteoarthrosis) was observed in the joints directly associated with these malformations.

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Lagier, R., Kaufmann, H. & Baud, C.A. Dyschondrosteosis (Léri-Weill Syndrome) observed in a VIth century skeleton. Skeletal Radiol. 3, 102–104 (1978). https://doi.org/10.1007/BF00363962

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  • DOI: https://doi.org/10.1007/BF00363962

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